Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis. Issue 5 (3rd October 2002)

• Record Type: Journal Article
• Authors: Reid, John K; Rees, Henrike; Cockcroft, Donald
• Is Part Of: Canadian respiratory journal. Volume 9:Issue 5(2002)
• Page Start: 342
• Page End: 346
• Publication Date: 2002-10-03
• Subjects: Angiomyolipoma -- Pulmonary lymphangioleiomyomatosis; Respiratory organs -- Diseases -- Periodicals; Respiration -- Canada -- Periodicals; Respiration; Respiratory organs -- Diseases; Canada; Respiratory Tract Diseases -- Periodicals; Periodicals; Periodicals; 616.2
• DOI: 10.1155/2002/958921
• Languages: English
• ISSNs: 1198-2241

Abstract

Abstract : A patient with pulmonary lymphangioleiomyomatosis was diagnosed more than 22 years after the onset of symptoms by a thoracoscopic lung biopsy, after a high resolution computerized tomogram of the chest was highly suggestive of the disease. After nearly 30 years since the onset of her symptoms, the patient leads a relatively normal life with only mildly abnormal lung function and has minimal reduction in her exercise tolerance. There have been few reports of patients surviving for such a long time after the onset of this disease; the literature suggests that most patients die within 15 years of symptom onset.