1. 2‐Methylcitric acid impairs glutamate metabolism and induces permeability transition in brain mitochondria. Issue 1 (15th February 2016) Authors: Amaral, Alexandre Umpierrez; Cecatto, Cristiane; Castilho, Roger Frigério; Wajner, Moacir Journal: Journal of neurochemistry Issue: Volume 137:Issue 1(2016) Page Start: 62 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
2. Acute lysine overload provokes marked striatum injury involving oxidative stress signaling pathways in glutaryl-CoA dehydrogenase deficient mice. (October 2019) Authors: Amaral, Alexandre Umpierrez; Seminotti, Bianca; da Silva, Janaína Camacho; de Oliveira, Francine Hehn; Ribeiro, Rafael Teixeira; Leipnitz, Guilhian; Souza, Diogo Onofre; Wajner, Moacir Journal: Neurochemistry international Issue: Volume 129(2019) Page Start: Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
3. Disturbance of mitochondrial functions provoked by the major long-chain 3-hydroxylated fatty acids accumulating in MTP and LCHAD deficiencies in skeletal muscle. (October 2016) Authors: Cecatto, Cristiane; Godoy, Kálita dos Santos; da Silva, Janaína Camacho; Amaral, Alexandre Umpierrez; Wajner, Moacir Journal: Toxicology in vitro Issue: Volume 36(2016) Page Start: 1 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
4. Disturbance of mitochondrial functions provoked by the major long-chain 3-hydroxylated fatty acids accumulating in MTP and LCHAD deficiencies in skeletal muscle. (October 2016) Authors: Cecatto, Cristiane; Godoy, Kálita dos Santos; da Silva, Janaína Camacho; Amaral, Alexandre Umpierrez; Wajner, Moacir Journal: Toxicology in vitro Issue: Volume 36(2016) Page Start: 1 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
5. High vulnerability of the heart and liver to 3‐hydroxypalmitic acid–induced disruption of mitochondrial functions in intact cell systems. Issue 9 (20th June 2018) Authors: Cecatto, Cristiane; Wajner, Alessandro; Vargas, Carmen Regla; Wajner, Simone Magagnin; Amaral, Alexandre Umpierrez; Wajner, Moacir Journal: Journal of cellular biochemistry Issue: Volume 119:Issue 9(2018) Page Start: 7678 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
6. Impairment of mitochondrial bioenergetics and permeability transition induction caused by major long-chain fatty acids accumulating in VLCAD deficiency in skeletal muscle as potential pathomechanisms of myopathy. (February 2020) Authors: Cecatto, Cristiane; Amaral, Alexandre Umpierrez; Roginski, Ana Cristina; Castilho, Róger Frigério; Wajner, Moacir Journal: Toxicology in vitro Issue: Volume 62(2020) Page Start: Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
7. Metabolite accumulation in VLCAD deficiency markedly disrupts mitochondrial bioenergetics and Ca2+ homeostasis in the heart. (25th March 2018) Authors: Cecatto, Cristiane; Amaral, Alexandre Umpierrez; da Silva, Janaína Camacho; Wajner, Alessandro; Schimit, Mariana de Oliveira Vargas; da Silva, Lucas Henrique Rodrigues; Wajner, Simone Magagnin; Zanatta, Ângela; Castilho, Roger Frigério; Wajner, Moacir Journal: FEBS journal Issue: Volume 285:Number 8(2018) Page Start: 1437 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
8. Mevalonolactone disrupts mitochondrial functions and induces permeability transition pore opening in rat brain mitochondria: Implications for the pathogenesis of mevalonic aciduria. (September 2017) Authors: Cecatto, Cristiane; Amaral, Alexandre Umpierrez; da Silva, Janaína Camacho; Wajner, Alessandro; Godoy, Kálita dos Santos; Ribeiro, Rafael Teixeira; Gonçalves, Aline de Mello; Vargas, Carmen Regla; Wajner, Moacir Journal: Neurochemistry international Issue: Volume 108(2017) Page Start: 133 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
9. Neuronal Death, Glial Reactivity, Microglia Activation, Oxidative Stress and Bioenergetics Impairment Caused by Intracerebroventricular Administration of D-2-hydroxyglutaric Acid to Neonatal Rats. (1st September 2021) Authors: Ribeiro, Rafael Teixeira; Seminotti, Bianca; Zanatta, Ângela; de Oliveira, Francine Hehn; Amaral, Alexandre Umpierrez; Leipnitz, Guilhian; Wajner, Moacir Journal: Neuroscience Issue: Volume 471(2021) Page Start: 115 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗
10. Pathogenesis of brain damage in glutaric acidemia type I: Lessons from the genetic mice model. Issue 78 (21st May 2019) Authors: Wajner, Moacir; Amaral, Alexandre Umpierrez; Leipnitz, Guilhian; Seminotti, Bianca Journal: International journal of developmental neuroscience Issue: Issue 78(2019:Nov.) Page Start: 215 Record Type: Journal Article View Content: Available online (eLD content is only available in our Reading Rooms) ↗