Organizing pneumonia as presenting feature of primary Sjögren's syndrome: A case report. (2023)

• Record Type: Journal Article
• Authors: Fernandez-Trujillo, Liliana; Morales, Eliana I.; Arias, Daniela; Zúñiga-Restrepo, Valeria; Sua, Luz F.
• Is Part Of: Respiratory medicine case reports. Volume 42(2023)
• Publication Date: 2023
• Subjects: Sjögren syndrome -- Organizing pneumonia -- Bronchoscopy -- Transbronchial biopsy -- Case report; Respiratory organs -- Diseases -- Periodicals; Chest -- Diseases -- Periodicals; Respiratory Tract Diseases -- Periodicals; Respiratory System -- Periodicals; Chest -- Diseases; Respiratory organs -- Diseases; Electronic journals; Periodicals; 616.2
• DOI: 10.1016/j.rmcr.2023.101830
• Languages: English
• ISSNs: 2213-0071

Abstract

Abstract: Sjögren's Syndrome (SS) is an autoimmune inflammatory disease, characterized by lymphocytic infiltration of exocrine glands. Approximately 10% of patients with SS have pulmonary involvement as the first manifestation of their disease, the most common being non-specific interstitial pneumonia. We present the case of a 51-year-old man with organizing pneumonia as the presenting feature of primary SS. Pulmonary involvement as the presenting feature of SS is uncommon, especially when the pattern on CT-scan is that of organized pneumonia. Initial management includes steroids and other immunosuppressants agents, with a better response in organized pneumonia secondary SS cases.