Can Isolated Discordant Atrioventricular Connections Survive Without Interatrial or Interventricular Shunt?. Issue 3 (May 2023)

• Record Type: Journal Article
• Authors: Kandachar, Pranav Subbaraya; Thomas, Eapen; Al Maskary, Areej; Campbell, Andrew
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 14:Issue 3(2023)
• Page Start: 387
• Page End: 389
• Publication Date: 2023-05
• Subjects: Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/21501351221145169
• Languages: English
• ISSNs: 2150-1351

Abstract

Clinical presentation of isolated discordant atrioventricular connections is akin to transposition of the great arteries. In the absence of a significant intracardiac shunt, profound cyanosis is expected at birth. We report one such 5-month-old infant who had only mild cyanosis. The left-sided tricuspid valve straddled the interventricular septum with a closed interventricular communication, a type of "Double Outlet Left Atrium with three atrioventricular valves, " which provided the necessary "left to right" shunt while severe regurgitation through the straddling part and a patent ductus arteriosus provided the effective pulmonary blood flow.