Recurrent pericardial effusion and tamponade in a patient with Erdheim-Chester disease (ECD). (24th November 2015)

• Record Type: Journal Article
• Authors: Mishra, Ajay Kumar; Mani, Sunithi; George, Anu Anna; Sudarsanam, Thambu David
• Is Part Of: BMJ case reports. Volume 2015
• Publication Date: 2015-11-24
• Subjects: Medicine -- Case studies -- Periodicals; 610.5
• DOI: 10.1136/bcr-2015-212483
• Languages: English
• ISSNs: 1757-790X

Abstract

Abstract : Erdheim-Chester disease (ECD) is a rare xanthogranulomatous disorder characterised by the proliferation of lipid laden histiocytes along with infiltration of various organs of the body. Although commonly presenting with bone pains secondary to bony infiltration, cardiac involvement in the form of periaortic fibrosis and pericardial involvement may be seen in a subgroup of patients. We report a case of ECD presenting as recurrent pericardial effusion along with pericardial tamponade.