Megacystis microcolon intestinal hypoperistalsis syndrome. (31st May 2013)

• Record Type: Journal Article
• Authors: Hiradfar, Mehran; Shojaeian, Reza; Dehghanian, Paria; Hajian, Sara
• Is Part Of: BMJ case reports. Volume 2013
• Publication Date: 2013-05-31
• Subjects: Medicine -- Case studies -- Periodicals; 610.5
• DOI: 10.1136/bcr-2012-007524
• Languages: English
• ISSNs: 1757-790X

Abstract

Abstract : Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a multisystemic disorder in which impaired intestinal motor activity causes recurrent symptoms of intestinal obstruction in the absence of mechanical occlusion, associated with bladder distention without distal obstruction of the urinary tract. MMIHS and prune belly syndrome may overlap in most of the clinical features and discrimination of these two entities is important because the prognosis, management and consulting with parents are completely different. MMIHS outcome is very poor and in this article we present two neonates with MMIHS that both died in a few days.