Cardiogenic shock in the context of newly diagnosed anomalous origin of the right coronary artery originating from the pulmonary artery: a case report. Issue 3 (31st March 2021)

• Record Type: Journal Article
• Authors: Kappel, Coralea; Chow, Justin; Ahmed, Zeeshan; Schwalm, Jon-David; Amin, Faizan
• Editors: Krupickova, Sylvia; Puricelli, Filippo; Houshmand, Golnaz; Camm, Christian Fielder; Kott, Katharine
• Is Part Of: European heart journal. Volume 5:Issue 3(2021)
• Publication Date: 2021-03-31
• Subjects: Congenital heart defect -- Atrial fibrillation -- Coronary vessel anomaly -- Coronary circulation -- Hemodynamics -- Coronary angiography -- Case report; Cardiology -- Periodicals; Cardiology -- Case studies -- Periodicals; Heart -- Diseases -- Periodicals; Heart -- Diseases -- Case studies -- Periodicals; 616.12
• DOI: 10.1093/ehjcr/ytab030
• Languages: English
• ISSNs: 2514-2119

Abstract

Abstract: Background: Anomalous right coronary artery (RCA) from the pulmonary artery (ARCAPA) is a rare congenital heart abnormality with varying clinical presentations, for which multiple imaging modalities are often required for diagnosis. Case summary: We present a case of a 76-year-old female presenting with 2 weeks of palpitations and shortness of breath who was found to be in rapid atrial fibrillation (AF) with congestive heart failure. Despite initial medical management, the patient developed cardiogenic shock with anuric renal failure. Emergent right and left heart catheterization did not demonstrate any significant obstructive coronary artery disease but showed severe right ventricular (RV) failure and raised the possibility of an ARCAPA. This diagnosis was further corroborated by findings on a subsequent transoesophageal echocardiogram. In view of profound decline and limited anticipated improvement, the patient ultimately decided to pursue comfort measures in a hospice setting. Discussion: We postulate that the underlying aetiology of our patient's shock state was multifactorial, notably progressive RCA-territory ischaemia and RV failure, sepsis, and new-onset uncontrolled AF. In adults, unrecognized congenital heart disease can uncommonly cause cardiogenic shock. In our case, echocardiography and invasive angiography were integrated for the diagnosis of ARCAPA given the clinical circumstances that limited the use of cardiac computed tomography angiography.