Intraabdominal Follicular Dendritic Cell Sarcoma: A Report of Three Cases and Review of the Literature. Issue 2 (March 2013)

• Record Type: Journal Article
• Authors: Urun, Yuksel; Kankaya, Duygu; Koral, Lokman; Yalcin, Bulent; Karabork, Ayca; Ceyhan, Koray; Boruban, Melih Cem; Utkan, Gungor; Demirkazik, Ahmet
• Is Part Of: Tumori. Volume 99:Issue 2(2013)
• Page Start: e65
• Page End: e69
• Publication Date: 2013-03
• Subjects: dendritic cell neoplasms -- follicular dendritic cell sarcoma; Cancer -- Periodicals; 616.994
• DOI: 10.1177/030089161309900231
• Languages: English
• ISSNs: 0300-8916

Abstract

Follicular dendritic cell sarcoma (FDCS) is a rare neoplasm that originates from follicular dendritic cells in lymphoid follicles. FDCS has been increasingly reported in recent years. However, data on FDCS are mostly based on single case reports or case series and its natural history and standard treatment are not clear. To increase the understanding of this rare disease, we report our experience of three cases of FDCS with an analysis of the morphological and immunophenotypic characteristics, clinical course, treatment options and response to treatment. In addition, we reviewed the literature on FDCS.