Focal portal vein stenosis in an adolescent potentially related to complicated umbilical catheter insertion in the neonatal period. Issue 4 (31st May 2013)

• Record Type: Journal Article
• Authors: Maleux, Geert; Hoffman, Ilse; Heye, Sam; Cassiman, David
• Is Part Of: Acta radiologica short reports. Volume 2:Issue 4(2013)
• Publication Date: 2013-05-31
• Subjects: Portal hypertension -- percutaneous intervention -- liver -- endoscopy -- stent; Radiology -- Periodicals; Radiology -- Case studies -- Periodicals; 616.075705
• DOI: 10.1177/2047981613492723
• Languages: English
• ISSNs: 2047-9816

Abstract

A 14-year-old girl, with no medical history except for a preterm birth at 7 months, presented with clinical and laboratory signs of pancytopenia. Radiological investigation, including abdominal ultrasound and magnetic resonance imaging revealed a focal irregular main portal vein wall and splenomegaly. Endoscopy showed major esophageal and gastric varices. Definitive diagnosis was made by direct, transhepatic portography revealing a focal stenosis associated with a dissection of the main portal vein. Percutaneous treatment including balloon angioplasty and stent placement resulted in complete re-expansion of the portal vein main branch. Clinical and radiological follow-up over 5 years showed complete disappearance of all clinical signs and normalization of laboratory data and splenic volume.