Epignathus Teratoma with Duplication of Mandible and Tongue: Report of a Case. (May 2013)

• Record Type: Journal Article
• Authors: Tsai, Yun-Ta; Cala-or, Ma. Arlene Cirineo; Lui, Chun-Chung; Wang, Tzu-Jou; Lai, Jui-Pin
• Is Part Of: Cleft palate-craniofacial journal. Volume 50:Number 3(2013)
• Page Start: 363
• Page End: 368
• Publication Date: 2013-05
• Subjects: bifid tongue -- duplication of mandible -- epignathus -- teratoma; Cleft palate -- Periodicals; Skull -- Abnormalities -- Periodicals; Cranial manipulation -- Periodicals; Skull -- Abnormalities -- Surgery -- Periodicals; Face -- Abnormalities -- Surgery -- Periodicals; Fente palatine -- Périodiques; Crâne -- Malformations -- Périodiques; Manipulation crânienne -- Périodiques; Crâne -- Malformations -- Chirurgie -- Périodiques; Face -- Malformations -- Chirurgie -- Périodiques; Cleft palate; Cranial manipulation; Face -- Abnormalities -- Surgery; Skull -- Abnormalities; Skull -- Abnormalities -- Surgery; Cleft Lip; Cleft Palate; Facial Bones -- abnormalities; Skull -- abnormalities; Periodicals; Periodicals; Periodicals; 617.522
• DOI: 10.1597/12-015
• Languages: English
• ISSNs: 1055-6656

Abstract

We report a female infant with presentation of epignathus teratoma involving duplication of both the mandible and tongue. Epignathus with duplication of the mandible has rarely been reported in the literature thus far. The location and extent of the tumor, as well as the involvement of adjacent structures, resulted in trismus and upper airway obstruction at birth. Thus, staged operations including debulking and correction of anatomical anomaly were performed on this patient after life-saving tracheostomy. As a result, we not only prevented morbidity associated with the anomaly but also refined the patient's appearance and improved her quality of life.