Pure Bladder Malignant Rhabdoid Tumor Successfully Treated With Partial Cystectomy, Radiation, and Chemotherapy: A Case Report and Review of the Literature. Issue 8 (November 2021)

• Record Type: Journal Article
• Authors: Assadi, Akram; Alzubaidi, Ahmad; Lesmana, Harry; Brennan, Rachel C.; Saad, Ali; Ortiz-Hernández, Vanessa; Gleason, Joseph M.
• Is Part Of: Journal of pediatric hematology/oncology. Volume 43:Issue 8(2021)
• Publication Date: 2021-11
• Subjects: rhabdoid tumor -- rare tumor -- bladder tumor -- bladder preserving surgery; Pediatric hematology -- Periodicals; Tumors in children -- Periodicals; 618.9215
• DOI: 10.1097/MPH.0000000000001963
• Languages: English
• ISSNs: 1077-4114

Abstract

Abstract : Background: Extracranial pure malignant rhabdoid tumors (MRT) are aggressive tumors that carry a poor prognosis. Bladder MRTs are very rare and only 8 cases have been reported previously. Observation: We present a case of a child with bladder MRT. Despite the aggressive nature of the bladder tumor, it was successfully treated with bladder-sparing surgery, adjuvant radiotherapy, and chemotherapy. Conclusions: Our case, and review of 8 previously reported cases, suggests that bladder MRT seems to behave less aggressively when compared with other extracranial MRTs, and bladder preserving surgery should be considered when feasible.