Calcolosi Reno-ureterale Nella Sindrome di V.A.C.T.E.R.L. Risoluzione Endourologica. Issue 22 (April 2013)

• Record Type: Journal Article
• Authors: Granelli, Pietro; Campobasso, Davide; Salsi, Paolo; Cretì, Giuseppe; Moretti, Matteo; Cisternino, Antonio; Frattini, Antonio; Ferretti, Stefania; Cortellini, Pietro
• Is Part Of: Urologia journal. Volume 80:Issue 22(2013)Supplement
• Page Start: 11
• Page End: 15
• Publication Date: 2013-04
• Subjects: VACTERL association -- Pediatric urolithiasis -- Endourology -- Sindrome di VACTERL -- Calcolosi pediatrica -- Endourologia; Urology -- Periodicals; 616.6005
• DOI: 10.5301/RU.2013.10616
• Languages: English
• ISSNs: 0391-5603

Abstract

Background: The endourological technique is a safe and effective approach in the treatment of large stones in the pediatric population with congenital malformations. Introduction: The VACTERL association is a group of congenital malformations that include vertebral defects, anal atresia, cardiac defects, tracheoesophageal fistula with atresia, renal defects, and radial upper limb dysplasia. Renal anomalies are found in approximately 90% of patients. Materials and Methods: We present a case of a 7-year-old girl with VACTERL association and cloacal malformations, undergoing multiple surgeries with subsequent Mitrofanoff continent appendico-vesicostomy. She presented at our attention for centimetric left ureteral and inferior pyelo-calyceal stones. She underwent flexible ureteroscopy with laser lithotripsy of both stones. A ureteral catheter and a nephrostomy tube have been left at the end of the procedure. Results: The ureteral catheter was removed in the 2nd post-operative day, the tubes were removed after a nephrostogram in the 8th post-operative day. The patient is stone-free. No complications were observed in the post-operative time. Conclusions: Endoscopy is the method of choice for the management of pediatric urolithiasis with complex renal calculi, due to its low incidence of major complications and a high stone-free rate.