Atypical, Extremely Rapid Growth of Pediatric Orbital Neurilemmoma. Issue 5 (September 2021)

• Record Type: Journal Article
• Authors: Vahdani, Kaveh; Luthert, Philip J.; Rose, Geoffrey E.
• Is Part Of: Ophthalmic plastic and reconstructive surgery. Volume 37:Issue 5(2021)
• Publication Date: 2021-09
• Subjects: Eye -- Surgery -- Periodicals; Ophthalmic plastic surgery -- Periodicals; Reconstructive Surgical Procedures -- Periodicals; Ophthalmologic Surgical Procedures -- Periodicals; Ophthalmology -- Periodicals; Surgery -- Periodicals; 617.70592
• DOI: 10.1097/IOP.0000000000001958
• Languages: English
• ISSNs: 0740-9303

Abstract

Abstract : Solitary orbital neurilemmoma—a benign tumor of Schwann cells in a peripheral nerve-sheath—are typically very slow growing and present in middle age; in the absence of neurofibromatosis, they are almost never seen in childhood. We describe the clinical presentation, imaging, pathology, and management of this tumor in a 12 years old—the tumor growing extremely rapidly over 5 months and without any evidence of cystic degeneration, hemorrhage, or sarcomatous features. The possibility of tumor growth having been accelerated by prior biopsy is discussed. Abstract : We report an adolescent with an extremely fast-growing solitary orbital schwannoma (neurilemmoma), the presentation, histology, and management of this possibly unique case being discussed.