ASYMPTOMATIC MULTIFOCAL PARACENTRAL ACUTE MIDDLE MACULOPATHY ASSOCIATED WITH JUVENILE DERMATOMYOSITIS: OPTICAL COHERENCE ANGIOGRAPHY FINDINGS. Issue Volume 15:Issues 5(2021) (September 2021)

• Record Type: Journal Article
• Authors: Starr, Matthew R.; Softing Hataye, Alaina L.; Bakri, Sophie J.
• Is Part Of: Retinal cases & brief reports. Volume 15:Issues 5(2021)
• Publication Date: 2021-09
• Subjects: juvenile dermatomyositis -- optical coherence tomography angiography -- paracentral acute middle maculopathy; Retina -- Diseases -- Periodicals; Retina -- Periodicals; Retinal Diseases -- Periodicals; Retina -- Case Reports; Retinal Diseases -- Case Reports; 617.7
• DOI: 10.1097/ICB.0000000000000849
• Languages: English
• ISSNs: 1935-1089

Abstract

Abstract : Purpose: To describe a unique presentation of multifocal paracentral acute middle maculopathy in a young patient with juvenile dermatomyositis including optical coherence tomography angiography findings. Methods: Retrospective single case report. Patient: Seventeen-year-old male patient with a history of juvenile dermatomyositis presented for routine hydroxychloroquine screening. Results: Optical coherence tomography revealed undulations of the outer retinal layers and retinal thinning near the fovea in both eyes. Optical coherence tomography angiography revealed loss of flow void densities in the superficial and deep capillary plexi in both eyes. These findings were consistent with a diagnosis of paracentral acute middle maculopathy. Conclusion: To the authors' knowledge, this is the first report of the optical coherence tomography angiography findings in paracentral acute middle maculopathy associated with juvenile dermatomyositis. The defects were located in the superficial and deep capillary plexi and likely due to the known occlusive retinopathy associated with juvenile dermatomyositis. Abstract : A 17-year-old, asymptomatic male patient with a history of juvenile dermatomyosis presented for a routine hydroxychloroquine screening. Optical coherence tomography revealed multifocal areas of outer retinal layer irregularities. Optical coherence tomography angiography revealed multiple flow density voids in the deep and superficial capillary plexi. The patient was diagnosed with paracentral acute middle maculopathy.