Risk assessment in scleroderma patients with newly diagnosed pulmonary arterial hypertension: application of the ESC/ERS risk prediction model. Issue 4 (18th October 2018)

• Record Type: Journal Article
• Authors: Mercurio, Valentina; Diab, Nermin; Peloquin, Grace; Housten-Harris, Traci; Damico, Rachel; Kolb, Todd M.; Mathai, Stephen C.; Hassoun, Paul M.
• Is Part Of: European respiratory journal. Volume 52:Issue 4(2018)
• Publication Date: 2018-10-18
• Subjects: Respiratory organs -- Diseases -- Periodicals; Respiration -- Periodicals; 616.2
• DOI: 10.1183/13993003.00497-2018
• Languages: English
• ISSNs: 0903-1936

Abstract

Pulmonary arterial hypertension (PAH) is characterised by sustained pulmonary vasoconstriction and remodelling of the pulmonary circulation leading to progressive right ventricular (RV) dysfunction. Although recent registry data suggest improving outcomes, PAH still carries a high morbidity and mortality burden [1]. The risk stratification model from current guidelines accurately predicts survival in scleroderma-associated PAH http://ow.ly/WmpN30lI5XF