Surgical considerations in cystic fibrosis: what every general surgeon needs to know. Issue 10 (3rd August 2022)

• Record Type: Journal Article
• Authors: Chetwood, John D.; Volovets, Anastasia; Sivam, Sheila; Koh, Cherry
• Is Part Of: ANZ journal of surgery. Volume 92:Issue 10(2022)
• Page Start: 2425
• Page End: 2432
• Publication Date: 2022-08-03
• Subjects: colorectal carcinoma -- cystic fibrosis -- distal intestinal obstruction syndrome -- intussusception -- pancreatitis; Surgery -- Periodicals; 617.005
• DOI: 10.1111/ans.17948
• Languages: English
• ISSNs: 1445-1433

Abstract

Abstract: Cystic fibrosis (CF) is a complex multiorgan disease, which often affects the gastrointestinal tract. With improved CF specific therapies and multidisciplinary management, patients with CF are now living longer with a median life expectancy of around 50 years. This increased life expectancy has resulted in corresponding increase in presentations of the CF patient with comorbid surgical conditions that were never important considerations. Investigations and management of these conditions, such as distal intestinal obstruction syndrome and colorectal cancer warrant good clinical understanding of the unique challenges that CF patients present including chronic immunosuppression, impaired respiratory function and their multi‐organ dysfunction. The purpose of this review is to provide general surgeons with a contemporary update on the CF related surgical issues as they are likely to become increasingly involved in the care of these complex patients and form an integral part of the multidisciplinary team. Abstract : The improved life expectancy for patients with cystic fibrosis means general surgeons will increasingly be involved in the care of such patients. Herein we provide a narrative, contemporary review on the management of surgical issues in this patient cohort.