Anesthetic Considerations for a Patient With Hereditary Hemorrhagic Telangiectasia (Osler–Weber–Rendu Syndrome) Undergoing a Five-Box Thoracoscopic Maze Procedure for Atrial Fibrillation. (8th October 2014)

• Record Type: Journal Article
• Authors: Robinson, Dominic; Rogers, Barbara; Kapoor, Ritu; Swan, Joseph; Speas, Gaylynn; Gutmann, Rebecca
• Is Part Of: Journal of investigative medicine high impact case reports. Volume 2:Number 4(2014)
• Publication Date: 2014-10-08
• Subjects: hereditary hemorrhagic telangiectasia -- Osler–Weber–Rendu syndrome -- five-box maze procedure -- arteriovenous malformation; Internal medicine -- Periodicals; Medical care -- Periodicals; 616.005
• DOI: 10.1177/2324709614553669
• Languages: English
• ISSNs: 2324-7096

Abstract

Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant genetic disorder involving the abnormal communication of vascular structures. HHT typically presents with recurrent epistaxis and telangiectasis of the nasal and buccal mucosa, tongue, and lips. More serious manifestations of this disease include cerebral, pulmonary, gastrointestinal, and hepatic arteriovenous malformations. This case report details a 55-year-old male with HHT undergoing a five-box maze procedure for curative treatment of atrial fibrillation. Particular anesthetic considerations are described to reduce morbidity and mortality in this patient population.