Rapunzel Syndrome Complicated by Escherichia coli Sepsis, Bowel Perforation, and Pancreatitis in an 11-year-old Malnourished Female. Issue 1 (24th February 2022)

• Record Type: Journal Article
• Authors: Daniel, Rhea; Arbuthnot, Mary; Ramireddy, Srinivas; Nair, Supriya
• Is Part Of: JPGN reports. Volume 3:Issue 1(2022)
• Page Start: e171
• Publication Date: 2022-02-24
• Subjects: Rapunzel syndrome -- trichobezoar -- sepsis -- pancreatitis; Pediatric gastroenterology -- Periodicals; Children -- Nutrition -- Periodicals; Children -- Nutrition; Pediatric gastroenterology; Infant Nutritional Physiological Phenomena; Child Nutritional Physiological Phenomena; Gastrointestinal Diseases; Infant; Child; Periodicals; Periodical; Case Reports; 618.9233
• DOI: 10.1097/PG9.0000000000000171
• Languages: English
• ISSNs: 2691-171X

Abstract

Abstract : The most common presenting symptoms of Rapunzel syndrome include abdominal pain (37%), nausea and vomiting (33.3%), obstruction (25.9%), and peritonitis (18.3%). Less commonly, patients may present with weight loss (7.4%) or intussusception (7.4%). Exceedingly rare complications of Rapunzel syndrome include gastric ulceration, obstructive jaundice, and acute pancreatitis as well as other malabsorptive-related complications including protein-losing enteropathy, iron deficiency, and megaloblastic anemia. This report details the case of an 11-year-old female with Rapunzel syndrome complicated by sepsis, a rare complication reported in only 2% of patients.