A case of progressive subcortical gliosis presenting clinically as Steele-Richardson-Olszewski syndrome. Issue 9 (September 1988)

• Record Type: Journal Article
• Authors: Will, R G; Lees, A J; Gibb, W; Barnard, R O
• Is Part Of: Journal of neurology, neurosurgery and psychiatry. Volume 51:Issue 9(1988)
• Page Start: 1224
• Page End: 1227
• Publication Date: 1988-09
• Subjects: Neurology -- Periodicals; Nervous system -- Surgery -- Periodicals; Psychiatry -- Periodicals; 616.8
• DOI: 10.1136/jnnp.51.9.1224
• Languages: English
• ISSNs: 0022-3050

Abstract

Abstract : A patient presenting with the characteristic clinical features of Steele-Richardson-Olszewski syndrome is described, in whom neuropathological examination revealed atypical features, including extensive cortical and subcortical gliosis. The clinical and pathological features are discussed with particular reference to Creutzfeldt-Jacob disease and it is proposed that the case should be classified as progressive subcortical gliosis.