Herlyn-Werner-Wunderlich (HWW) syndrome with kyphoscoliosis: a rare urogenital anomaly in a teenage girl. Issue 3 (22nd March 2021)

• Record Type: Journal Article
• Authors: Jhirwal, Manisha; Singh, Pratibha; Sharma, Charu; Khera, Pushpinder
• Is Part Of: BMJ case reports. Volume 14:Issue 3(2021)
• Publication Date: 2021-03-22
• Subjects: obstetrics and gynaecology -- musculoskeletal and joint disorders -- radiology (diagnostics); Medicine -- Case studies -- Periodicals; 610.5
• DOI: 10.1136/bcr-2020-238688
• Languages: English
• ISSNs: 1757-790X

Abstract

Abstract : The obstructed haemivagina with ipsilateral renal agenesis (OHVIRA) syndrome also known as Herlyn-Werner-Wunderlich syndrome, a rare congenital malformation in females, results due to developmental abnormality in the müllerian duct. We are reporting a case of a 14-year-old girl who presented with pain and a lump in abdomen for the last 5 months. The MRI abdomen and pelvis confirmed the diagnosis of OHVIRA syndrome. The patient underwent haematocolpos and haematometra drainage, followed by vaginal septum resection.