A surgical case of primary perivascular epithelioid cell tumor of the heart. Issue 7 (2nd June 2020)

• Record Type: Journal Article
• Authors: Daimon, Masahiro; Kanki, Sachiko; Ozawa, Hideki; Katsumata, Takahiro
• Is Part Of: Journal of cardiac surgery. Volume 35:Issue 7(2020)
• Page Start: 1732
• Page End: 1735
• Publication Date: 2020-06-02
• Subjects: cardiac tumor -- PEComa; Heart -- Surgery -- Periodicals; 617.412005
• DOI: 10.1111/jocs.14676
• Languages: English
• ISSNs: 0886-0440

Abstract

Abstract: Background: We encountered an extremely rare case of perivascular epithelioid cell tumor (PEComa) of the heart. Case Report: A 54‐year‐old woman was admitted to our hospital because a solid mass developing in the left atrioventricular groove by computed tomography scans of the chest. Histologic examination of the resected tumor revealed that the tumor had proliferating fusiform or spheroid cells with clear cytoplasm. Immunostaining showed positive results for α‐smooth muscle actin, a myogenic marker, and human melanin black‐45 (HMB‐45), leading to a diagnosis of PEComa. The patient was discharged uneventfully, and there was no recurrence for the last thirteen years postoperatively. Conclusions: We experienced a surgical case of PEComa primarily occurring in the heart. Although no sign of a recurrence is observed to date, we consider it necessary to follow up the case carefully.