A rare childhood case of Behcet's disease and chronic thromboembolic pulmonary hypertension. Issue 7 (17th May 2020)

• Record Type: Journal Article
• Authors: Wang, Amy S.; Rosenzweig, Erika B.; Takeda, Koji
• Is Part Of: Journal of cardiac surgery. Volume 35:Issue 7(2020)
• Page Start: 1669
• Page End: 1672
• Publication Date: 2020-05-17
• Subjects: aorta and great vessel -- behcet's disease -- pulmonary hypertension -- pulmonary thromboendarterectomy; Heart -- Surgery -- Periodicals; 617.412005
• DOI: 10.1111/jocs.14610
• Languages: English
• ISSNs: 0886-0440

Abstract

Abstract: Background: Pulmonary embolism and chronic thromboembolic pulmonary hypertension (CTEPH) are rare complications of Behcet's disease, especially in pediatric patients. Aims/Methods/Results/Conclusions: This case report highlights a presentation of CTEPH in an adolescent with Behcet's disease. A multidisciplinary approach was required for managing this patient's CTEPH, which successfully reversed the patient's pulmonary hypertension.