Vascular Malformation and Common Keratinocytic Nevus of the Soft Type: Phacomatosis Pigmentovascularis Revisited. (20th November 2014)

• Record Type: Journal Article
• Authors: Laureano, André; Carvalho, Rodrigo; Amaro, Cristina; Freitas, Isabel; Cardoso, Jorge
• Other Names: Jimbow Kowichi Academic Editor.
• Is Part Of: Case reports in dermatological medicine. Volume 2014(2014)
• Publication Date: 2014-11-20
• Subjects: Dermatology -- Periodicals; Skin -- Diseases -- Periodicals; 616.5005
• DOI: 10.1155/2014/437085
• Languages: English
• ISSNs: 2090-6463

Abstract

Abstract : Phacomatosis pigmentovascularis is a rare syndrome characterized by the coexistence of a pigmented nevus and a cutaneous vascular malformation. We report a 5-year-old boy with all the typical findings of phacomatosis pigmentovascularis type Ia. Although its existence according to the traditional classification has been questioned, this case represents a very rare association of a capillary vascular malformation and a common keratinocytic nevus of the soft type.