Bowel perforation from malignant atrophic papulosis treated with eculizumab. Issue 1 (2nd January 2021)

• Record Type: Journal Article
• Authors: Sathiyaraj, Ajithraj; Jayakumar, Priyanga; McGlennon, Matthew R.; Eckford, John F.; Anne, Sandy Itwaru
• Is Part Of: Proceedings. Volume 34:Issue 1(2021)
• Page Start: 111
• Page End: 113
• Publication Date: 2021-01-02
• Subjects: Bowel perforation -- Degos disease -- eculizumab -- malignant atrophic papulosis; Medicine -- Periodicals; Medicine; Medicine -- Periodicals; Periodicals; Electronic journals; 616.005
• DOI: 10.1080/08998280.2020.1809942
• Languages: English
• ISSNs: 0899-8280

Abstract

Abstract: We present the case of a 57-year-old man with known cutaneous manifestations of malignant atrophic papulosis, also known as Köhlmeier-Degos disease, who developed an almost-fatal small bowel perforation following a parathyroidectomy. He required two surgical interventions during his initial hospitalization and was started on eculizumab. Despite these therapies, the patient developed recurrent bowel perforations and ultimately died.