Managing Harlequin Syndrome in VA-ECMO – do not forget the right ventricle. (July 2022)

• Record Type: Journal Article
• Authors: Wilson, James; Fisher, Richard; Caetano, Francisca; Soliman-Aboumarie, Hatem; Patel, Brijesh; Ledot, Stephane; Price, Susanna; Vandenbriele, Christophe
• Is Part Of: Perfusion. Volume 37:Number 5(2022)
• Page Start: 526
• Page End: 529
• Publication Date: 2022-07
• Subjects: Harlequin syndrome -- right ventricular failure -- VA-ECMO -- mechanical circulatory support -- septic cardiomyopathy; Perfusion (Physiology) -- Periodicals; Blood -- Circulation, Artificial -- Periodicals; Heart -- Surgery -- Periodicals; Extracorporeal Circulation -- Periodicals; Perfusion -- Periodicals; Circulation extracorporelle -- Périodiques; Perfusion -- Périodiques; 617.41
• DOI: 10.1177/02676591211020895
• Languages: English
• ISSNs: 0267-6591

Abstract

Harlequin Syndrome (also known as North-South Syndrome) is a complication of veno-arterial extracorporeal membrane oxygenation (V-A ECMO) that can occur when left ventricular function starts to recover. While most commonly due to continued impaired gas exchange in the lungs, we present a case caused by right ventricular dysfunction, successfully managed by conversion of the ECMO circuit to a veno-veno-arterial (VV-A) configuration.