Basilar impression complicating osteogenesis imperfecta type IV: the clinical and neuroradiological findings in four cases. Issue 3 (1st March 1999)

• Record Type: Journal Article
• Authors: Hayes, M; Parker, G; Ell, J; Sillence, D
• Is Part Of: Journal of neurology, neurosurgery and psychiatry. Volume 66:Issue 3(1999)
• Page Start: 357
• Page End: 364
• Publication Date: 1999-03-01
• Subjects: basilar impression -- osteogenesis imperfecta; Neurology -- Periodicals; Nervous system -- Surgery -- Periodicals; Psychiatry -- Periodicals; 616.8
• DOI: 10.1136/jnnp.66.3.357
• Languages: English
• ISSNs: 0022-3050

Abstract

Abstract : OBJECTIVES: To describe the clinical and neuroradiological features of basilar impression in patients with osteogenesis imperfecta type IV. METHODS: Four patients with basilar impression were ascertained in a population study of osteogenesis imperfecta. All four had detailed clinical and neuroradiological examination with both CT and MRI of the craniocervical junction andposterior fossa structures. RESULTS: All four showed significant compression of the posterior fossa structures and surgical decompression was performed with relief of symptoms. CONCLUSION: Symptoms of cough headache and trigeminal neuralgia occurring in patients with osteogenesis imperfecta are indications for detailed clinical and neuroradiological investigation to document basilar impression.