Non-operative management of a splenic laceration in a patient with the Proteus syndrome. Issue 2 (March 1997)

• Record Type: Journal Article
• Authors: Ceelen, W; De Waele, J; Kunnen, M; de Hemptinne, B
• Is Part Of: Journal of accident & emergency medicine. Volume 14:Issue 2(1997)
• Page Start: 111
• Page End: 113
• Publication Date: 1997-03
• Subjects: Emergency medicine -- Periodicals; 616.025
• DOI: 10.1136/emj.14.2.111
• Languages: English
• ISSNs: 2633-6138

Abstract

Abstract : An adult patient with the Proteus syndrome sustained a grade III splenic laceration after falling off a horse. Clinical features of this rare disorder include subcutaneous and visceral hamartomatous tumours. The patient also suffered from chronic intravascular coagulation associated with extensive haemangiomatosis (Kasabach-Merritt syndrome). Considering the visceral anomalies and abnormal coagulation, a non-operative approach was preferred despite considerable transfusion requirement, and the patient successfully underwent embolisation of the splenic artery. This is the first reported case of splenic injury in a patient with Proteus syndrome.