Challenges in Obstetric Anesthesia in a Parturient With Native American Myopathy: A Case Report. Issue 12 (10th December 2021)

• Record Type: Journal Article
• Authors: Mock, Sean; Jabaut, Joshua; Barra, David; Angelo, Tiffany; Benjamin, John
• Is Part Of: A & A practice. Volume 15:Issue 12(2020)
• Page Start: e01541
• Publication Date: 2021-12-10
• Subjects: Analgesia -- Periodicals; Analgesia -- Case studies -- Periodicals; Anesthesiology -- Periodicals; Anesthesiology -- Case studies -- Periodicals; 617.9605
• DOI: 10.1213/XAA.0000000000001541
• Languages: English
• ISSNs: 2575-3126

Abstract

Abstract : Native American Myopathy (NAM) is an inherited, malignant hyperthermia-susceptible myopathy associated with abnormal craniofacial development and neuromuscular scoliosis. There is scant NAM anesthetic literature and, to our knowledge, no existing publications describing the anesthetic management of a NAM parturient. The constellation of symptoms of NAM in the parturient presents a number of challenges to the obstetric anesthesiologist, including difficult airway associated with craniofacial abnormalities and pregnancy, malignant hyperthermia susceptibility, and possible difficult neuraxial block. In this report, we present the anesthetic management of a parturient with NAM and previous extensive posterior spinal fusion undergoing cesarean delivery under general anesthesia.