Selective agenesis of pancreatic isthmus parenchyma with preservation of main pancreatic duct continuity, a very rare entity: Case report. (2015)

• Record Type: Journal Article
• Authors: Paiella, Salvatore; De Pastena, Matteo; Esposito, Alessandro; Salvia, Roberto; Morigi, Consuelo; Bassi, Claudio
• Is Part Of: International journal of surgery case reports. Volume 6(2015)
• Page Start: 169
• Page End: 171
• Publication Date: 2015
• Subjects: Pancreatic anomaly -- Dorsal pancreatic agenesis -- Agenesis of pancreatic isthmus -- IPMN -- BD-IPMN; Surgery -- Periodicals; Surgical Procedures, Operative -- Periodicals; Surgery; Electronic journals; Periodicals; 617.005
• DOI: 10.1016/j.ijscr.2014.09.023
• Languages: English
• ISSNs: 2210-2612

Abstract

Highlights: Pancreatic congenital anomalies are not infrequent. A rare selective agenesis of pancreatic parenchyma is presented. Neoplastic lesions should always been considered in case of pancreatic congenital anomalies. Abstract: Context: Agenesis of the dorsal pancreas is a rare anomaly, mostly associated with other medical conditions. It may be complicated with pancreatic neoplasms. Case report: We report the case of a 51-year-old male with selective agenesis of pancreatic isthmus with preservation of main pancreatic duct and branch-duct intraductal papillary mucinous neoplasm (BD-IPMN) with suspicious features of the pancreas. Conclusion: This is probably the first report of isolated agenesis of pancreatic isthmus with conservation of main pancreatic duct.