Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases. Issue 1 (January 2022)

• Record Type: Journal Article
• Authors: Lei, Shaoyang; Gui, Shaogao; Zhang, Haixu; Wang, Yanxia; Liu, Ronghui; Ye, Yufang; Zhang, Shuqian; Fan, Bing
• Is Part Of: Journal of international medical research. Volume 50:Issue 1(2022)
• Publication Date: 2022-01
• Subjects: Poland syndrome -- syndactyly -- thoracic wall -- multidetector computed tomography -- pectoral muscle -- breast -- hand deformity; Medicine -- Periodicals; Pharmacology -- Periodicals; 610.5
• DOI: 10.1177/03000605211069485
• Languages: English
• ISSNs: 0300-0605

Abstract

Poland syndrome is a rare congenital developmental deformity characterized by unilateral agenesis or hypoplasia of thoracic wall soft tissue. We report two adult cases of Poland syndrome detected by computed tomography (CT) images. CT images of the two cases depicted an asymmetric chest wall with the absence of a breast and agenesis of the pectoralis muscles. A physical examination of case 1 showed a thin right chest wall with depression of the right nipple region. Hand deformities were also observed, including brachydactyly and syndactyly. In case 2, hand deformities were not found in a physical examination. Using multi-planar reconstruction, the size, position, origin, and termination of bilateral pectoral muscles could be compared symmetrically. For patients with Poland syndrome, a timely diagnosis and treatment are important. The use of chest CT in clinical practice could play an important role in the early diagnosis and treatment of Poland syndrome.