Hypoplastic right retro-oesophageal aortic arch: similarities to interrupted aortic arch. Issue 6 (December 1989)

• Record Type: Journal Article
• Authors: Knight, W B
• Is Part Of: Heart. Volume 62:Issue 6(1989)
• Page Start: 477
• Page End: 481
• Publication Date: 1989-12
• Subjects: Heart -- Diseases -- Treatment -- Periodicals; Cardiology -- Periodicals; 616.12
• DOI: 10.1136/hrt.62.6.477
• Languages: English
• ISSNs: 1355-6037

Abstract

Abstract : At echocardiography a dysmorphic neonate was found to have a hypoplastic mitral valve, left ventricle, and ascending aorta with interruption of the aortic arch between the left common carotid and the left subclavian arteries--the left subclavian artery arose from a normal sized left descending aorta. Cardiac catheterisation and subsequent necropsy confirmed this arrangement but also showed a tortuous right retro-oesophageal aortic arch. This arch was severely hypoplastic distal to the right subclavian artery. These cardiovascular anomalies occurred in the child of a family in which other members showed the velo-cardio-facial syndrome, a condition known to be associated with right aortic arch. This aortic arch arrangement may be impossible to distinguish from simple aortic interruption by echocardiography alone.