Relapsing cerebral amyloid angiopathy-related inflammation: the wax and the wane. Issue 5 (24th June 2017)

• Record Type: Journal Article
• Authors: Salam, Sharfaraz; Anandarajah, Mayooreshan; Al-Bachari, Sarah; Pal, Piyali; Sussman, Jonathan; Hamdalla, Hisham
• Is Part Of: Practical neurology. Volume 17:Issue 5(2017)
• Page Start: 392
• Page End: 395
• Publication Date: 2017-06-24
• Subjects: cerebral amyloid angiopathy related inflammation cerebrovascular disease; Neurology -- Periodicals; 616.8005
• DOI: 10.1136/practneurol-2017-001599
• Languages: English
• ISSNs: 1474-7758

Abstract

Abstract : Cerebral amyloid angiopathy-related inflammation (CAA-I) is a rare variant of cerebral amyloid angiopathy (CAA). Its precise pathophysiology remains uncertain and we currently have limited evidence on which immunosuppressive agents are the most effective in its treatment. The disease course of CAA-I disorders can vary from an isolated clinical event to recurrent episodes. We present a case of biopsy-confirmed CAA-I that gives insight into its potential relapsing nature and the challenges of its long-term management.