540 Perinatal (Fetal And Neonatal) Diagnosis and Evolution of Cardiac Tumours. (October 2012)

• Record Type: Journal Article
• Authors: Dimitiru, L; Dimitiru, AG; Stamatin, M
• Is Part Of: Archives of disease in childhood. Volume 97(2012)Supplement 2
• Page Start: A157
• Page End: A157
• Publication Date: 2012-10
• Subjects: Children -- Diseases -- Periodicals; Infants -- Diseases -- Periodicals; 618.920005
• DOI: 10.1136/archdischild-2012-302724.0540
• Languages: English
• ISSNs: 0003-9888

Abstract

Abstract : Cardiac tumors are rarely symptomatic and highlighted in the fetus when the size and position do not interfere with intracardiac hemodynamic. Objectives. To present four cases of cardiac tumors, confirmed by Doppler echocardiography (Echo) performed in the first 14 days postnatal, 2 of which were already highlighted by fetal echocardiogtaphy. Cases presentation. Fetal echocardiography showed 3 and respetivelly 4 intracardiac mass, well circumscribed, oval, 6–12 mm diameter, with echogenic appearance increased from normal cardiac structure, located in the IVS and the posterior wall of the LV, slightly protrudes in the lumen but no significant obstruction of LV outflow tract. Postnatal Echo confirmed the fetal echocardiography diagnosis multiple cardiac rhabdomyama. ECG: no suggestive changes. Chest X-Ray: cardiomegaly. One of cases was later diagnosed with tuberous sclerosis Bourneville. Fetal echocardiography not extracardiac changes detected in this case. The three cases of rhabdomyoma evolved according to age, without major cardiac distress and while echocardiography showed mild involution of tumors size without complete disappearance In the fourth case, Echo in the neonatal period revealed atrioventricular septal defect with intracardiac masses, 2 of 3 pedicled, non obstructive, pleading for a multiple cardiac fibroma. Not cardiac arrhythmias were detected fetal and postnatal development. Conclusions. fetal ultrasound screening and especially at older age of pregnancy may reveal the presence of cardiac tumors, mainly rhabdomyoama, then confirmed by Echo postnatal. Monitoring these tumors both in utero and post natal to allow early detection of obstructive disorders, with sometimes severe cardiac distress and requiring cardiovascular surgery.