Reversible steatohepatosis in a young boy with brittle type 1 diabetes mellitus: mauriac syndrome. (20th July 2011)

• Record Type: Journal Article
• Authors: Shrivastava, Makardhwaj Sarvadaman; Palkar, Atul Vijay; Padwal, Namita J; Moulick, Nivedita
• Is Part Of: BMJ case reports. Volume 2011
• Publication Date: 2011-07-20
• Subjects: Medicine -- Case studies -- Periodicals; 610.5
• DOI: 10.1136/bcr.03.2011.3975
• Languages: English
• ISSNs: 1757-790X

Abstract

Abstract : A 14-year-old male, diagnosed case of type 1 diabetes mellitus since 1 year, presented with uncontrolled blood glucose levels, non-compliance with insulin therapy and recurrent admissions with diabetic ketoacidosis. His blood glucose levels were difficult to control with wide fluctuations in insulin requirement. He had absent secondary sexual characteristics and hepatomegaly. Liver biopsy showed macrovesicularsteatosis without fibrosis or inflammation. Many glycogenated nuclei were present. He was started on intensive insulin therapy, whereby he showed subsequent regression of hepatomegaly and onset of pubertal spurt.