Complex Repair of a Completely Fused Nullicuspid Aortic Valve Late in Adolescence. Issue 6 (November 2021)

• Record Type: Journal Article
• Authors: Meza, James M.; Nellis, Joseph R.; Rankin, J. Scott; Wolsky, Ryan M.; Badhwar, Vinay; Hughes, G. Chad; Turek, Joseph W.
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 12:Issue 6(2021)
• Page Start: 790
• Page End: 793
• Publication Date: 2021-11
• Subjects: Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/21501351211017854
• Languages: English
• ISSNs: 2150-1351

Abstract

We report a case of an 18-year-old female who presented with severe aortic stenosis and insufficiency, eight years following resection of a subaortic membrane. On echocardiography, she was found to have a completely fused or nullicuspid valve, with three equal sinuses and three commissural fusions. Aortic valve repair included leaflet tricuspidization, three commissurotomies, trileaflet ring annuloplasty, and pericardial leaflet reconstruction. At one year follow-up, the patient is asymptomatic, with stable gradients.