Rare provisional entity: primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma in a young woman. Issue 6 (27th May 2008)

• Record Type: Journal Article
• Authors: Csomor, J; Bognár, Á; Benedek, S; Sinkó, J; Fekete, S; Krenács, L; Matolcsy, A; Reiniger, L
• Is Part Of: Journal of clinical pathology. Volume 61:Issue 6(2008)
• Page Start: 770
• Page End: 772
• Publication Date: 2008-05-27
• Subjects: Pathology -- Periodicals; Pathology, Molecular -- Periodicals; 616.0705
• DOI: 10.1136/jcp.2007.054585
• Languages: English
• ISSNs: 0021-9746

Abstract

Abstract : Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma is a rare and provisional entity, characterised by cutaneous involvement and aggressive clinical behaviour. The case is here presented of a young woman with concurrent cutaneous and systemic involvement. Despite multi-agent chemotherapy, only partial remission could be achieved, and the patient died from therapy-resistant respiratory and circulatory failure. This case report is intended to add to the data collected on this rare entity, with only about 20 cases as yet described.