Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery. (16th June 2021)

• Record Type: Journal Article
• Authors: Nagamatsu, Yuki; Goda, Ayumi; Ito, Junnosuke; Takeuchi, Kaori; Kikuchi, Hanako; Kariyasu, Toshiya; Machida, Haruhiko; Inami, Takumi; Kohno, Takashi; Soejima, Kyoko; Satoh, Toru
• Is Part Of: ESC heart failure. Volume 8:Number 4(2021)
• Page Start: 3427
• Page End: 3430
• Publication Date: 2021-06-16
• Subjects: Unilateral absence of a pulmonary artery -- Pulmonary hypertension -- 4D computed tomography -- Upfront triple combination therapy; Heart failure -- Periodicals; 616.129005
• DOI: 10.1002/ehf2.13459
• Languages: English
• ISSNs: 2055-5822

Abstract

Abstract: We report the case of a 64‐year‐old female diagnosed with severe pulmonary hypertension due to the unilateral absence of a pulmonary artery. The four‐dimensional computed tomography scan is a useful modality for revealing detailed anatomical findings for differential diagnoses and surgical decision‐making. The patient had severe pulmonary hypertension with a mean pulmonary artery pressure (PAP) of 74 mmHg and was treated with triple upfront combination therapy, leading to significant improvement in pulmonary haemodynamics (to 27 mmHg in mean PAP) and functional capacity (WHO functional class, from III to II; 6‐min walk distance, from 211 to 276 m).