Simultaneous LeFort III and LeFort I Osteotomies in Craniometaphyseal Dysplasia. (November 2021)

• Record Type: Journal Article
• Authors: Chan, Christopher; Garg, Ravi; Wlodarczyk, Jordan R.; Yen, Stephen; Urata, Mark M.
• Is Part Of: Cleft palate-craniofacial journal. Volume 58:Number 12(2021)
• Page Start: 1560
• Page End: 1568
• Publication Date: 2021-11
• Subjects: craniometaphyseal dysplasia -- craniofacial surgery -- simultaneous LeFort III and LeFort I -- orthognathic surgery; Cleft palate -- Periodicals; Skull -- Abnormalities -- Periodicals; Cranial manipulation -- Periodicals; Skull -- Abnormalities -- Surgery -- Periodicals; Face -- Abnormalities -- Surgery -- Periodicals; Fente palatine -- Périodiques; Crâne -- Malformations -- Périodiques; Manipulation crânienne -- Périodiques; Crâne -- Malformations -- Chirurgie -- Périodiques; Face -- Malformations -- Chirurgie -- Périodiques; Cleft palate; Cranial manipulation; Face -- Abnormalities -- Surgery; Skull -- Abnormalities; Skull -- Abnormalities -- Surgery; Cleft Lip; Cleft Palate; Facial Bones -- abnormalities; Skull -- abnormalities; Periodicals; Periodicals; Periodicals; 617.522
• DOI: 10.1177/1055665621990942
• Languages: English
• ISSNs: 1055-6656

Abstract

Craniometaphyseal dysplasia (CMD) is a rare genetic disease affecting bone metabolism with sclerosis of craniofacial bones. Orthognathic surgery has rarely been described in this patient population due to the bony thickness, making osteotomies challenging. We present a 19-year-old male with CMD with malocclusion, severe midface hypoplasia, and obstructive sleep apnea. With the aid virtual planning, we safely performed a combined LeFort III/I midface advancement to correct a negative overjet to improve occlusal balance, decrease scleral show, and diminish daytime sleepiness.