Retroperitoneal Extrarenal Angiomyolipomas: An Evidence-Based Approach to a Rare Clinical Entity. (8th August 2012)

• Record Type: Journal Article
• Authors: Minja, Emmanuel J.; Pellerin, Megan; Saviano, Nicole; Chamberlain, Ronald S.
• Other Names: Kavukcu S. Academic Editor.; Sulowicz W. Academic Editor.; Zuo L. Academic Editor.
• Is Part Of: Case reports in nephrology. Volume 2012(2012)
• Publication Date: 2012-08-08
• Subjects: Nephrology -- Periodicals; Kidneys -- Diseases -- Periodicals; Nephrology; Kidneys -- Diseases; Nephrology; Periodicals; Electronic journals; Periodicals; 616.61
• DOI: 10.1155/2012/374107
• Languages: English
• ISSNs: 2090-6641

Abstract

Abstract : Extrarenal angiomyolipomas (ERAMLs) are rare tumors that present as incidentalomas upon imaging for other conditions. Retroperitoneal ERAMLs present a unique challenge from a diagnostic and treatment standpoint as they can mimic other benign and malignant retroperitoneal tumors. We present a case of a 39-year-old female with a 19.3 cm × 13.5 cm × 10.7 cm left extrarenal retroperitoneal mass. Histopathologic examination and HMB-45 staining revealed the mass to be a retroperitoneal ERAML. Our case report provides a comprehensive literature review and an evidence-based algorithm for taking care of patients with ERAMLs.