Marfan Syndrome: A Case Report. (4th December 2012)

• Record Type: Journal Article
• Authors: Ganesh, Rajendran; Vijayakumar, Rajendran; Selvakumar, Haridoss
• Other Names: Chen Y.-K. Academic Editor.; Delbem A. C. B. Academic Editor.
• Is Part Of: Case reports in dentistry. Volume 2012(2012)
• Publication Date: 2012-12-04
• Subjects: Dentistry -- Case studies -- Periodicals; Oral medicine -- Case studies -- Periodicals; Oral Medicine; Dentistry; Dentistry; Oral medicine; Electronic journals; Periodical; Case studies; Periodicals; Case Reports; Fulltext; Internet Resources; Periodicals; 617.6
• DOI: 10.1155/2012/595343
• Languages: English
• ISSNs: 2090-6447

Abstract

Abstract : Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially the skeleton, lungs, eyes, heart, and the large blood vessel that distributes blood from the heart to the rest of the body. A case report of Marfan syndrome has been reported with oral features. The dental problems of the child were treated under general anesthesia and a one-month review showed intact stainless steel crowns' restorations and no signs of secondary caries.