Malignant Peripheral Nerve Sheath Tumor of the Small Bowel: An Unusual Presentation with Fatal Outcome. (28th August 2013)

• Record Type: Journal Article
• Authors: Mohtaram, Amina; Mesmoudi, Siham; M'rabti, Hind; Rami, Amal; Latib, Rachida; Bernoussi, Zakia; Aaribi, Imane; Ben Ameur El Youbi, Meryam; Errihani, Hassan
• Other Names: Chichareon S. B. Academic Editor.; Yokoyama Y. Academic Editor.
• Is Part Of: Case reports in oncological medicine. Volume 2013(2013)
• Publication Date: 2013-08-28
• Subjects: Oncology -- Periodicals; Tumors -- Periodicals; Oncology -- Case studies -- Periodicals; Neoplasms; Oncology; Tumors; Electronic journals; Periodicals; Case studies; Periodicals; Case Reports; Fulltext; Internet Resources; Periodicals; 616.994
• DOI: 10.1155/2013/423867
• Languages: English
• ISSNs: 2090-6706

Abstract

Abstract : Malignant peripheral nerve sheath tumor of the small bowel is an extremely rare disease. Histologic distinction from other types of soft tissue sarcoma especially fibrosarcoma and leiomyosarcoma requires electron microscopy. Complete surgery remains the only curative treatment. However, late diagnosis makes curative surgery more difficult. The contribution of chemotherapy to incomplete surgery has been proved without controlled studies. We report a case of this type of lesion discovered following a small bowel perforation.