Primary angiitis of the central nervous system mimicking a cerebellar tumor. (4th May 2021)

• Record Type: Journal Article
• Authors: Zhang, Guodong; Yang, Chunxia; Chang, Jinjin; Yuan, Xunhui; Bai, Yun'an; Niu, Jianyi; Wang, Meiying
• Is Part Of: British journal of neurosurgery. Volume 35:Number 3(2021)
• Page Start: 367
• Page End: 369
• Publication Date: 2021-05-04
• Subjects: Primary angiitis of the central nervous system -- tumor-like -- granulomatous vasculitis -- lymphocytic vasculitis; Nervous system -- Surgery -- Periodicals; 617.48
• DOI: 10.1080/02688697.2018.1464122
• Languages: English
• ISSNs: 0268-8697

Abstract

Abstract: Primary angiitis of the central nervous system (PACNS), is a rare and poorly understood disease mainly characterized by multifocal segmental inflammation of the small and medium vessels of the central nervous system. Most PACNS are multiple lesions, occurring in the supratentorial subcortical and deep white matter, and only a few cases present as a tumor-like mass lesion. Herein, we describe an extremely rare case of PACNS occurred in the cerebellum, which mimicked a cerebellar tumor. To the best of our knowledge, this is the first reported case of cerebellar tumor-like PACNS proved by histopathological examination.