Dermatofibrosarcoma protuberans (DFSP) in children: A combined multidisciplinary approach. Issue 1 (11th November 2020)

• Record Type: Journal Article
• Authors: Sleiwah, Aseel; Psomadakis, Cristina; Craythorne, Emma; Stefanato, Catherine M.; Rickaby, William; Robson, Alistair; Mellerio, Jemima E.; Greig, Aina
• Is Part Of: Pediatric dermatology. Volume 38:Issue 1(2021)
• Page Start: 233
• Page End: 236
• Publication Date: 2020-11-11
• Subjects: cutaneous surgery -- dermatofibrosarcoma -- dermatopathology -- neoplasms -- skin; Pediatric dermatology -- Periodicals; Children -- Diseases -- Periodicals; 618.925
• DOI: 10.1111/pde.14425
• Languages: English
• ISSNs: 0736-8046

Abstract

Abstract: Dermatofibrosarcoma protuberans (DFSP) is rare, comprising (1%‐6%) of all sarcomas. The incidence is less than one per million before the age of 20. It is a locally aggressive tumor with a low risk of metastasis. We share our experience in the management of three pediatric patients with complex cases of DFSP in a combined surgical approach involving plastic and dermatologic surgery, using the slow Mohs micrographic surgery technique.