Cardiac Paraganglioma in a 14-Year-Old. Issue 3 (May 2021)

• Record Type: Journal Article
• Authors: Bansal, Neha; Walters, Henry L.; Aggarwal, Sanjeev
• Is Part Of: World journal for pediatric & congenital heart surgery. Volume 12:Issue 3(2021)
• Page Start: 433
• Page End: 436
• Publication Date: 2021-05
• Subjects: Pediatric cardiology -- Periodicals; Congenital heart disease in children -- Periodicals; Heart -- Abnormalities -- Surgery -- Periodicals; Heart -- Surgery -- Periodicals; Heart Defects, Congenital -- surgery -- Periodicals; Cardiac Surgical Procedures -- Periodicals; Child -- Periodicals; Adult -- Periodicals; 618.9212
• DOI: 10.1177/2150135118824077
• Languages: English
• ISSNs: 2150-1351

Abstract

Cardiac paraganglioma (PGL) is a rare catecholamine-secreting tumor forming 1% to 3% of cardiac tumors. Although most PGL occur sporadically, evidence exists that 40% of them may be related to familial cancer predisposition syndromes. We present a unique case of a 14-year-old female who presented with persistent hypertension and was found to have a cardiac PGL. During surgical resection, even though the main right coronary was preserved, the sinoatrial (SA) nodal artery was surrounded by the tumor and required resection with the tumor. The patient subsequently developed SA node dysfunction and is currently being evaluated for placement of a permanent pacemaker.