A Case of Myoclonus–Dystonia Responding to Low-frequency Pallidal Stimulation. (5th May 2017)

• Record Type: Journal Article
• Authors: Sarva, Harini; Miravite, Joan; Swan, Matthew C.; Deik, Andres; Raymond, Deborah; Severt, William Lawrence; Kopell, Brian H.
• Editors: Louis, Elan D.
• Is Part Of: Tremor and other hyperkinetic movements. Volume 7(2017)
• Publication Date: 2017-05-05
• Subjects: Myoclonus–dystonia -- deep brain stimulation -- low-frequency stimulation; Tremor -- Periodicals; Hyperkinesia -- Periodicals; 616.8
• DOI: 10.7916/D82Z1BS4
• Languages: English
• ISSNs: 2160-8288

Abstract

Background: High-frequency pallidal stimulation has been shown to improve various types of dystonia, including myoclonus-dystonia. Case Report: We report a case of epsilon sarcoglycan mutation-negative myoclonus–dystonia with response to low-frequency bilateral pallidal stimulation. Discussion: Low-frequency pallidal stimulation provides an effective means of treating various dystonias, regardless of genetic status, as in our case, as it provides increased programming options with fewer adverse effects.