Carpal Tunnel Syndrome Associated with Klippel-Trénaunay-Weber Syndrome: A Case Report. Issue 2 (April 2015)

• Record Type: Journal Article
• Authors: Siegall, Evan; Ratner, Joshua
• Is Part Of: JBJS case connector. Volume 5:Issue 2(2015)
• Publication Date: 2015-04
• Subjects: Orthopedic surgery -- Case studies -- Periodicals; Orthopedic surgery -- Periodicals; Orthopedics; Orthopedic Procedures; Orthopedic surgery; Periodicals; Electronic journals; Case studies; Periodicals; 616.7
• DOI: 10.2106/JBJS.CC.N.00133
• Languages: English
• ISSNs: 2160-3251

Abstract

Abstract : Case: A fourteen-year old patient with Klippel-Trénaunay-Weber syndrome presented with an eleven-year history of pain and subjective weakness in the median nerve distribution of the hand. Electromyography studies demonstrated chronic denervation, and magnetic resonance imaging ruled out vascular malformations as a cause of extrinsic compression. Despite the chronic compression of the median nerve within the carpal tunnel and known complications associated with Klippel-Trénaunay-Weber syndrome, a surgical release was performed. Conclusion: Postoperatively, the patient noted immediate pain relief. At the time of the three-year follow-up, the subjective strength and function of the hand were greatly improved compared with the preoperative status. Even with symptoms suggesting decade-long compression, carpal tunnel release can be a safe and beneficial treatment for patients with Klippel-Trénaunay-Weber syndrome.