Left heart matters in Ebstein's anomaly: the importance of a closer follow up—a case report. Issue 4 (29th June 2020)

• Record Type: Journal Article
• Authors: Ordoñez, Maria Victoria; Bedair, Radwa; Curtis, Stephanie L
• Editors: Garg, Pankaj; Abumuaileq, Rami Riziq Yousef; Refaat, Marwan; von Klemperer, Kate; Mukherjee, Rahul; Green, Peregrine
• Is Part Of: European heart journal. Volume 4:Issue 4(2020)
• Page Start: 1
• Page End: 5
• Publication Date: 2020-06-29
• Subjects: Ebstein's anomaly -- Tricuspid regurgitation -- Left ventricular outflow obstruction (LVOTO) -- Case report; Cardiology -- Periodicals; Cardiology -- Case studies -- Periodicals; Heart -- Diseases -- Periodicals; Heart -- Diseases -- Case studies -- Periodicals; 616.12
• DOI: 10.1093/ehjcr/ytaa077
• Languages: English
• ISSNs: 2514-2119

Abstract

Abstract: Background: Ebstein's anomaly (EA) is mainly thought of as a right heart condition, however, congenital left-sided lesions can co-exist. Therefore, it is paramount to include the left side of the heart as part of a routine investigation in these patients. We present a 57-year-old symptomatic patient with EA and progressive tricuspid regurgitation (TR) associated with acquired left ventricular outflow obstruction (LVOTO). Case summary: A 57-year-old women, known to have severe EA presented with shortness of breath and chest pain on exertion secondary to progression of the tricuspid valve regurgitation and right ventricle dilatation leading to a dynamic compression of the left outflow tract requiring surgical intervention. Discussion: Left ventricular obstruction secondary to severe TR and dilation of the right ventricle can present and remain silent at rest but becoming significant on exertion. Therefore, we recommend that all patients with EA and significant TR undergo exercise echocardiography at regular intervals to specifically look for acquired dynamic LVOTO.