Resection of a Thoracic Hemangioblastoma in a Patient With Von Hippel-Lindau: 3-Dimensional Operative Video. Issue 3 (13th July 2018)

• Record Type: Journal Article
• Authors: Dekker, Simone E; Ostergard, Thomas A; Glenn, Chad A; Shammassian, Berje; Cox, Efrem; Pace, Jonathan A; Yoo, Kevin; Alonso, Fernando; Bambakidis, Nicholas C
• Is Part Of: Operative neurosurgery. Volume 16:Issue 3(2019)
• Page Start: 395
• Page End: 395
• Publication Date: 2018-07-13
• Subjects: Thoracic laminectomy -- Thoracic hemangioblastoma -- 3D operative video -- Von Hippel-Lindau; Nervous system -- Surgery -- Periodicals; 617.480590
• DOI: 10.1093/ons/opy178
• Languages: English
• ISSNs: 2332-4252

Abstract

Abstract: This 3-dimensional operative video illustrates resection of a thoracic hemangioblastoma in a 30-year-old female with a history of Von Hippel-Lindau disease. The patient presented with right lower extremity numbness and flank pain. Magnetic resonance imaging (MRI) demonstrated an enhancing intradural intramedullary lesion at T 7 consistent with a hemangioblastoma. The patient underwent a thoracic laminectomy with a midline dural opening for tumor resection. This case demonstrates the principles of intradural intramedullary spinal cord tumor resection. In this particular case, internal debulking was untenable owing to the vascular nature of hemangioblastomas. The operative video demonstrates en bloc tumor removal. Postoperative MRI demonstrated gross total resection. The postoperative course was uneventful. The natural history of this disease, treatment options, and potential complications are discussed.