A case of severe aortic stenosis caused by unicuspid unicommissural aortic valve. Issue 4 (October 2020)

• Record Type: Journal Article
• Authors: Tanabe, Junya; Sato, Hirotomo; Endo, Akihiro; Yoshitomi, Hiroyuki; Shimizu, Koji; Oda, Teiji; Tanabe, Kazuaki
• Is Part Of: Journal of cardiology cases. Volume 22:Issue 4(2020)
• Page Start: 170
• Page End: 173
• Publication Date: 2020-10
• Subjects: Unicuspid aortic valve -- Aortic valve stenosis -- Aortic aneurysm -- Intracranial aneurysm; Cardiology -- Periodicals; Cardiovascular Diseases -- Case Reports; Cardiovascular Diseases -- Periodicals; Cardiology -- Case Reports; Cardiology -- Periodicals; Cardiology; Electronic journals; Periodicals; 616.12
• DOI: 10.1016/j.jccase.2020.05.015
• Languages: English
• ISSNs: 1878-5409

Abstract

Abstract: Unicuspid aortic valve (UAV) is an extremely rare congenital malformation that frequently presents with valvular dysfunction or aortic aneurysm. Here we report the case of a 49-year-old man with severe aortic stenosis caused by UAV requiring the Bentall procedure. Two- and three-dimensional transesophageal echocardiography revealed an eccentric opening in an aortic valve and a lateral attachment to the aorta at the orifice level, suggestive of which is consistent with unicommissural UAV as confirmed by surgical findings. <Learning objective: We report a rare case of unicuspid aortic valve (UAV) requiring the Bentall procedure. This case demonstrates the utility of two- and three-dimensional transesophageal echocardiography in revealing the morphology of UAV, as confirmed by surgical findings.>