Impact of Interdisciplinary Team Care for Children With 22q11.2 Deletion Syndrome. (December 2020)

• Record Type: Journal Article
• Authors: Hickey, Scott E.; Kellogg, Brian; O'Brien, Meghan; Hall, Courtney; Kirschner, Richard E.; Santoro, Stephanie L.; Leonard, Hayley; Baylis, Adriane L.
• Is Part Of: Cleft palate-craniofacial journal. Volume 57:Number 12(2020)
• Page Start: 1362
• Page End: 1369
• Publication Date: 2020-12
• Subjects: 22q11.2 deletion syndrome -- velocardiofacial syndrome -- DiGeorge syndrome -- guidelines; Cleft palate -- Periodicals; Skull -- Abnormalities -- Periodicals; Cranial manipulation -- Periodicals; Skull -- Abnormalities -- Surgery -- Periodicals; Face -- Abnormalities -- Surgery -- Periodicals; Fente palatine -- Périodiques; Crâne -- Malformations -- Périodiques; Manipulation crânienne -- Périodiques; Crâne -- Malformations -- Chirurgie -- Périodiques; Face -- Malformations -- Chirurgie -- Périodiques; Cleft palate; Cranial manipulation; Face -- Abnormalities -- Surgery; Skull -- Abnormalities; Skull -- Abnormalities -- Surgery; Cleft Lip; Cleft Palate; Facial Bones -- abnormalities; Skull -- abnormalities; Periodicals; Periodicals; Periodicals; 617.522
• DOI: 10.1177/1055665620947985
• Languages: English
• ISSNs: 1055-6656

Abstract

Objective: To evaluate disease-specific guideline adherence among children with 22q11.2 deletion syndrome receiving multidisciplinary team care through a 22q specialty clinic compared to children not receiving team care. Design: Retrospective chart review; quality improvement project. Setting: Tertiary care pediatric hospital. Patients: One hundred eighty-nine patients with 22q11.2 deletion syndrome were categorized into those receiving team care and those not receiving team care. Guideline adherence was compared between the 2 groups. Main Outcome Measure(s): Percent adherence across 8 disease-specific guidelines. Results: A Welch t test revealed mean adherence among patients receiving team care was significantly higher (83% vs 42%, P < .001) compared those not receiving team care. Among team patients with a single 22q Center visit, a paired samples t test showed that mean adherence increased from 63% before the clinic encounter to 86% six months after the encounter ( P < .001). Some guidelines were more likely to be associated with provider nonadherence, whereas others were more likely to be associated with patient nonadherence. Conclusions: Multidisciplinary team care is associated with significantly higher guideline adherence in children with 22q11DS. Additional research is needed to investigate the effect of team care on long-term health outcomes in children with 22q11DS.